Hemihydranencephaly is a severe cephalic disorder characterized by complete or almost complete absence of one hemisphere of the cerebral cortex with preservation of meninges, basal ganglia, pons, medulla, cerebellum, and falx. It is a special type of hydranencephaly. It is a very rare disease. As it stands, only 9 cases have been reported. Cognitive and language functions may be largely or totally normal, although motor function deficits in one half of the body are typical.
References
Greco F, Finocchiaro M, Pavone P, Trifiletti RR, Parano E. Hemihydranencephaly: case report and literature review. J Child Neurol. 2001;16 :218–221
